Dyke-Davidoff-Masson syndrome: A case report from South India
Keywords:
Seizures, Hemiplegia, Hemiatrophy, Mental Retardation
Abstract
Dyke-Davidoff-Masson Syndrome (DDMS) is a rare disease in Indian subcontinent. It is more common in western countries. DDMS is characterized by seizures, facial asymmetry, contralateral hemiplegia and mental retardation. Characteristic radiological features are cerebral hemiatrophy with homolateral hypertrophy of skull and sinuses. We report a case of DDMS in a 9 year old girl who presented with seizures, Developmental delay in motor and speech domains, spastic hemiparesis of left upper and lower limb and MRI revealed characteristic features diagnostic of DDMS .
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References
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2. Ono K, Komai K, Ikeda T. Dyke Davidoff-Masson Syndrome manifested by seizure in late childhood: A case report. J Clin Neurosci. 2003;10:367–71. [PubMed]
3. Amann B, Garcia de la Iglesia C, Mckenna P, Pomarol-Clotet E, Sanchez-Guerra M, Orth M. Treatment- refractory Schizoaffective disorder in a patient with Dyke-Davidoff Masson Syndrome. CNS Spectr. 2009;14(1):36–39. [PubMed]
4. Dyke CG, Davidoff LM, Masson CB. Cerebral hemiatrophy with homolateral hypertrophy of the skull and sinus. Surg Gynecol Obstet. 1933; 57: 588-600.
5. Solomon GE, Hilak SK, Gold AP, Carter S. Natural history of acute hemiplegia of childhood. Brain. 1970; 93(1) : 107-120. [PubMed]
6. Sener RN, Jinkins JR,MR of craniocerebral hemiatrophy. Clin Imaging. 1992Apr-Jun;16(2):93-7. [PubMed]
7. Zilkha A. CT of cerebral hemiatrophy. AJR Am J Roentgenol. 1980 Aug;135(2):259-62. [PubMed]
8. Aquiar PH, Liu CW, Leitao H, Issa F, Lepski G, Figueiredo EG, et al. MR and CT imaging in Dyke-Davidoff-Masson syndrome. Report of three cases and contribution to pathogenesis and differential diagnosis. Arq Neuropsiquiatr 1998 Dec;56(4):803-7. [PubMed]
9. Rao KCVG. Degenerative diseases and hydrocephalus. In: Lee SH, Rao KDVG, Zimmerman RA, editors. Cranial MRI and CT. Fourth edition.New York: Mc Graw - Hill; 1999.p.212 – 214. [PubMed]
10. Narain NP, Kumar R,Narain P. Dyke-Davidoff-Masson syndrome. Indian Pediatr. 2008 Nov;45(11):927. [PubMed]
CITATION
DOI: 10.17511/ijpr.2016.i09.02
Published: 2016-09-30
How to Cite
Dr. Sowjan. M, Dr. Vikram.R, Dr. Rajakumar.P.G., & Dr. Mohammad Ali. (2016). Dyke-Davidoff-Masson syndrome: A case report from South India. Pediatric Review: International Journal of Pediatric Research, 3(9), 646-648. https://doi.org/10.17511/ijpr.2016.i09.02
Section
Case Report
Copyright (c) 2016 Author (s). Published by Siddharth Health Research and Social Welfare Society
This work is licensed under a Creative Commons Attribution 4.0 International License.
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