Rapidly progressing juvenile scleroderma: A case report
Keywords:
Juvenile systemic sclerosis, Arthritis, Juvenile Scleroderma
Abstract
Juvenile Scleroderma encompasses a range of conditions unified by the presence of fibrosis of the skin. Juvenile scleroderma is of two major types: Juvenile localized scleroderma and Juvenile Systemic sclerosis. Juvenile localized scleroderma is the predominant type seen in children (>95%). We report a case of systemic sclerosis in a child, which is associated with higher mortality and morbidity. Apart from the characteristic mask like face, arthritis was the predominant complaint in our case.
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References
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2. Scalapino K, Arkachaisri T, Lucas M, Fertig N, Helfrich DJ, Londino AV, Jr, Steen VD, Medsger TA., Jr Childhood onset systemic sclerosis: classification, clinical and serologic features, and survival in comparison with adult onset disease. J Rheu-matol. 2006;33(5):1004–1013.
3. Martini G, Foeldvari I, Russo R, Cuttica R, Eberhard A, Ravelli A, Lehman TJ, de Oliveira SK, Susic G, Lyskina G, et al. Systemic sclerosis in childhood: clinical and immunologic features of 153 patients in an international database. Arthritis Rheum. 2006;54(12): 3971–3978. DOI: https://doi.org/10.1002/art.22207
4. Zulian F, Athreya BH, Laxer R, Nelson AM, Feitosa de Oliveira SK, Punaro MG, Cuttica R, Higgins GC, Van Suijlekom-Smit LW, Moore TL, et al. Juvenile-localized scleroderma: clinical and epidemiological features in 750 children. Aninter-national study. Rheu-matology (Oxford) 2006; 45(5): 614-620.DOI: https: // doi.org/10.1093/ rheumatology/ kei251
5. A Yadav, TP Yadav, V Gupta. Juvenile Systemic Sclerosis. Journal of Indian Academy of Clinical Medicine, 2011; 12( 2): 128-33
6. Fleischmajer R, Perlish JS, Reeves JRT. Cellular infiltrates in scleroderma skin. Arthritis Rheum1977; 20:975-984.doi:https://doi.org/10.1002/art. 1780200410
7. Nietert PJ, Sutherland SE, Silver RM, et al. Is occupational organic solvent exposure a risk factor for scleroderma? Arthritis Rheum 1998; 41: 1111-18: doihttps: //doi. org/10.1002/1529-0131(199806)41: 6<1111:: AID-ART19>3.0.CO;2-J
8. Robert M, Kleigman, Bonita, Stanton, Joseph St.G, Schor NF. Neslon Textbook of Pediatrics. 20thedition. Philadelphia: Elsevier Health;2015
CITATION
DOI: 10.17511/ijpr.2018.i06.07
Published: 2018-06-30
How to Cite
Dr. Zalak Shah, & Dr. Dhanya Soodhana Mohan. (2018). Rapidly progressing juvenile scleroderma: A case report. Pediatric Review: International Journal of Pediatric Research, 5(6), 339-342. https://doi.org/10.17511/ijpr.2018.i06.07
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Section
Case Report
Copyright (c) 2018 Author (s). Published by Siddharth Health Research and Social Welfare Society
This work is licensed under a Creative Commons Attribution 4.0 International License.
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