4Dimensional XStrain echocardiographic assessment by sequential chamber analysis of Double Outlet Left Ventricular with Tricuspid Atresia.

4D XStrain TTE evaluation of DOLV

  • Akhil Mehrotra Prakash Heart Station Niralanagar Lucknow
  • Swati Singh
  • Shubham Kacker
Keywords: Double outlet left ventricle with tricuspid atresia, tricuspid atresia, D-malposition of great arteries, Atrial Septal Defect, Ventricular septal Defect


Double outlet left ventricle (DOLV) is as an extremely rare cyanotic congenital cardiac malformation with an incidence of less than 1 in 200,000 live births, and usually manifests during the neonatal period. DOLV occurs most commonly in the form of atrial situs solitus with atrioventricular (AV) concordance but is often associated with myriads of cardiac anomalies such as VSD, ASD, PDA, pulmonary stenosis, right ventricular hypoplasia, and tricuspid atresia (TA). The clinical manifestations depend largely on the type of the associated cardiac defects, e.g. pulmonary or aortic outflow tract obstruction, resulting from pulmonary or aortic valve stenosis respectively. We are presenting an exceedingly rare case report of DOLV, tricuspid atresia, D-malposition of great arteries, mild pulmonary stenosis with absence of RV hypoplasia. Assessed by sequential chamber analysis, employing 4Dimensional XStrain color Doppler echocardiography. This is one of the rarest of rare case report.


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How to Cite
Mehrotra, A., Singh, S., & Kacker, S. (2022). 4Dimensional XStrain echocardiographic assessment by sequential chamber analysis of Double Outlet Left Ventricular with Tricuspid Atresia . Pediatric Review: International Journal of Pediatric Research, 9(4). Retrieved from https://pediatrics.medresearch.in/index.php/ijpr/article/view/724
Case Report