4Dimensional XStrain echocardiographic assessment by sequential chamber analysis of Double Outlet Left Ventricular with Tricuspid Atresia.
Keywords:
Double outlet left ventricle with tricuspid atresia, tricuspid atresia, D-malposition of great arteries, Atrial Septal Defect, Ventricular septal Defect
Abstract
Double outlet left ventricle (DOLV) is an extremely rare cyanotic congenital cardiac malformationwith an incidence of less than 1 in 200,000 live births and usually manifests during the neonatalperiod. DOLV occurs most commonly in the form of atrial situs solitus with atrioventricular (AV)concordance but is often associated with myriads of cardiac anomalies such as VSD, ASD, PDA,pulmonary stenosis, right ventricular hypoplasia, and tricuspid atresia (TA). The clinicalmanifestations depend largely on the type of the associated cardiac defects, e.g. pulmonary or aorticoutflow tract obstruction, resulting from pulmonary or aortic valve stenosis respectively. We arepresenting an exceedingly rare case report of DOLV, tricuspid atresia, D-malposition of greatarteries, and mild pulmonary stenosis with the absence of RV hypoplasia, assessed by sequentialchamber analysis, employing 4Dimensional XStrain colour Doppler echocardiography.
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References
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18. DeLeon SY, Ow EP, Chiemmongkoltip P, Vitullo DA, Quinones JA, Fisher EA, et al. Alternatives in biventricular repair of double-outlet left ventricle. Ann Thorac Surg 1995; 60:213-6.
19. Chiavarelli M, Boucek MM, Bailey LL. Arterial correction of double outlet left ventricle by pulmonary artery translocation. Ann Thorac Surg 1991; 53:1098-100.
20. Huhta JC, Hagler DJ, Seward JB, Tajik AJ, Julsrud PR, Ritte DG. Two dimensional echocardiographic assessment of dextrocardia: A segmental approach. AM J Cardiol 1982; 50:1351-60.
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22. Muraru D, Niero A, Zanella HR, Cherata D, Badano LP. Three-dimensional speckle-tracking Echocardiography: Benefits and limitations of integrating myocardial mechanics with three dimensional imaging. Cardiovasc. Diagn. Ther, 2018; 8: 101-117.
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24. Takahashi K, Naami GA, Thompson R, Inage A, Mackie AS, Smallhorn JF, Normal Rotational, torsion and untwisting data in children, adolescents and young adults. J Am Soc Echocardiogr. 2010; 23:286-93.
2. Manner J, Seidl W, Steiding G: Embryological observations on the formal pathogenesis of double-outlet left ventricle with a right ventricular infundibulum. Thoracic cardiovasc Surg 1997; 45:172-177.
3. Van Praagh R, Weinberg PM, Srebro J: Double-outlet left ventricle. In Moss’ Heart Disease in infants, children, and Adolescents. Edited by Adams FH, Emmanouilides GC, Reimenschneider JA. Baltimore: Williams & Wilkins; 1989:461-485.
4. Wilkinson J: Double outlet ventricle. In pediatric Cardiology. Vol 2. Edited by Anderson RH, Macartney FJ, Shinebourne EA, Tynan M. Ediburg: Churchill living stone; 1987:889-911.
5. Sakakibara, S., Takao, A., Hashimoto, A., and Nogi, M. Both great vessels arising from the left ventricle. Bulletin of the Heart Institute Japan, 1967:66-86.
6. Lilje C, Weiss F, Lacour- Gayer F, et al Images in cardiovascular medicine. Double-outlet Left Ventricle. Circulation 2007, 115(3):e36-e37.
7. Bharati S, Lev M, Stewart R, McAllister HA, Kirklin JW. The morphologic spectrum of double outlet left ventricle and its surgical significance. Circulation 1978; 58: 558-65.
8. Otero Coto E, Quero Jimenez M, Castaneda AR, Rufilanchas JJ, Deverall PB. Double outlet from chamber of left ventricular morphology. Br Heart J 1979, 42:15-21.
9. Gouton M, Bozio A, Rey C, et al: Double outlet left ventricle: a rare and unusual cardiopathy. Apropos of 7 new cases [in French]. Arch Mal Coeur Vaiss 1966, 89:553-559.
10. Donald Jr H, William E. Double outlet left ventricle, In: Adams FH, Emmanouilides GL, Riemen-schneider TA, eds. Heart Diseases in Infants Children and Adolescents. 5th ed. Baltimore: Williams and Wilkins, 1995, 1270-6.
11. Mohan JC, Agarwala R, Arora R. Double outlet left ventricle with intact ventricular septum; a cross-sectional and Doppler echocardiographic diagnosis. Intern J Cardiol 1991; 33:447-9.
12. Rocha IEG, Pazin IC, Loops LM: Tricuspid atresia and double outlet left ventricle: A rare association in adulthood. Arq Bras Cardiol: Imagem cardiovasc. 2017; 30:31-35.
13. Alehan D, Dogan OF, Ozkutlu S: Echocardiographic diagnosis of an extremetly rare case with double-outlet left ventricle, tricuspid atresia and two balanced ventricles: Pediatr Cardiol 2007; 28: 418-419.
14. Vaseenon T, Diehl AM, Mattioli L: Tricuspid atresia with double outlet left
Ventricle and bilateral conus. Chest. 1978; 74: 676-9.
15. Lopes LM, Tamac P, Rangel N, Soraggi AMB, Furlanetto BHS, Furlanetto G: Double outlet left ventricle. Echocardiographic diagnosis: Arq Bras Cardiol. 2001; 76:514-6.
16. McElhinney DB, Reddy VM, Hanley FL. Pulmonary root translocation for biventricular repair of double-outlet left ventricle with absent subpulmonic conus. J Thorac Cardiovasc Surg. 1997; 114:501-3.
17. Hagler D, Double-outlet right ventricle and double outlet left ventricle. In Moses and Adams’, Heart Disease in infants, children and adolescents vol 2, edn 7, Phildelphia: Lipppincott Willams & Witkins: 2008:1100-1127.
18. DeLeon SY, Ow EP, Chiemmongkoltip P, Vitullo DA, Quinones JA, Fisher EA, et al. Alternatives in biventricular repair of double-outlet left ventricle. Ann Thorac Surg 1995; 60:213-6.
19. Chiavarelli M, Boucek MM, Bailey LL. Arterial correction of double outlet left ventricle by pulmonary artery translocation. Ann Thorac Surg 1991; 53:1098-100.
20. Huhta JC, Hagler DJ, Seward JB, Tajik AJ, Julsrud PR, Ritte DG. Two dimensional echocardiographic assessment of dextrocardia: A segmental approach. AM J Cardiol 1982; 50:1351-60.
21. Galal O, Hatle L, AL Halees Z. Changes of management in a patient with double outlet left ventricle. Cardiol young 1999; 9:602-605.
22. Muraru D, Niero A, Zanella HR, Cherata D, Badano LP. Three-dimensional speckle-tracking Echocardiography: Benefits and limitations of integrating myocardial mechanics with three dimensional imaging. Cardiovasc. Diagn. Ther, 2018; 8: 101-117.
23. Carreras F, Garcia-Barnes J, Gil D, Pujadas S, Li CH, Suarez-Arias R, Leta R, Alomar X, Ballester M, Pons-Llado G. Left ventricular torsion and longitudinal shortening: two fundamental components of myocardial mechanics assessed by tagged cine-MRI in normal subjects. Int J Cardiovasc Imaging. 2012; 28: 273-84.
24. Takahashi K, Naami GA, Thompson R, Inage A, Mackie AS, Smallhorn JF, Normal Rotational, torsion and untwisting data in children, adolescents and young adults. J Am Soc Echocardiogr. 2010; 23:286-93.
How to Cite
Akhil Mehrotra, Swati Singh, & Shubham Kacker. (2022). 4Dimensional XStrain echocardiographic assessment by sequential chamber analysis of Double Outlet Left Ventricular with Tricuspid Atresia . Pediatric Review: International Journal of Pediatric Research, 9(4), 14-20. Retrieved from https://pediatrics.medresearch.in/index.php/ijpr/article/view/724
Section
Case Report
Copyright (c) 2022 Author (s). Published by Siddharth Health Research and Social Welfare Society
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