4Dimensional XStrain echocardiographic assessment by sequential chamber analysis of Double Outlet Left Ventricular with Tricuspid Atresia.

  • Akhil Mehrotra Chief, Non-Invasive Cardiologist, Pediatric and Adult Cardiology, Prakash Heart Station, D-16, Nirala Nagar, Lucknow, U.P, India.
  • Swati Singh Senior Echocardiography Technician, Pediatric and Adult Cardiology, Prakash Heart Station, D-16, Nirala Nagar, Lucknow, U.P, India
  • Shubham Kacker Senior coordinator, Project Management Office, Tech Mahindra, Noida, U.P, India
Keywords: Double outlet left ventricle with tricuspid atresia, tricuspid atresia, D-malposition of great arteries, Atrial Septal Defect, Ventricular septal Defect


Double outlet left ventricle (DOLV) is an extremely rare cyanotic congenital cardiac malformationwith an incidence of less than 1 in 200,000 live births and usually manifests during the neonatalperiod. DOLV occurs most commonly in the form of atrial situs solitus with atrioventricular (AV)concordance but is often associated with myriads of cardiac anomalies such as VSD, ASD, PDA,pulmonary stenosis, right ventricular hypoplasia, and tricuspid atresia (TA). The clinicalmanifestations depend largely on the type of the associated cardiac defects, e.g. pulmonary or aorticoutflow tract obstruction, resulting from pulmonary or aortic valve stenosis respectively. We arepresenting an exceedingly rare case report of DOLV, tricuspid atresia, D-malposition of greatarteries, and mild pulmonary stenosis with the absence of RV hypoplasia, assessed by sequentialchamber analysis, employing 4Dimensional XStrain colour Doppler echocardiography.


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How to Cite
Akhil Mehrotra, Swati Singh, & Shubham Kacker. (2022). 4Dimensional XStrain echocardiographic assessment by sequential chamber analysis of Double Outlet Left Ventricular with Tricuspid Atresia . Pediatric Review: International Journal of Pediatric Research, 9(4), 14-20. Retrieved from https://pediatrics.medresearch.in/index.php/ijpr/article/view/724
Case Report