Double-Chambered Right Ventricle with Large Apical VSD- a Rare Case Report
Double-chambered right ventricle (DCRV) is a rare condition seen in only 0.5 - 2.0% of all cases ofcongenital heart disease (CHD). An isolated DCRV is very rare, while approximately 80-90% ofDCRV cases are associated with various other congenital heart defects, with VSD, in particular, aperimembranous type VSD, being the most common. In DCRV right ventricle is separated into aproximal high-pressure and distal low-pressure chamber. It can be caused either by the presence ofan anomalous muscle bundle (AMB), by hypertrophy of endogenous trabecular tissue, oroccasionally by an aberrant moderator band. DCRV is characterised by intraventricular pressuregradients greater than 20 mmHg, turbulent flow patterns in the ventricle, and increased pulmonaryblood flow. Currently, the methods for detection of DCRV with VSD are Colour echocardiography,Cardiac catheterization, Cardiac CT and Cardiac MRI. This anomaly is often diagnosed duringchildhood and adolescence, while very few are found in adults. Here, we are presenting anextremely rare case report of a 7-month-old male child afflicted with symptomatic DCRV, unusuallyassociated with a large apical muscular VSD.
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