Hydranencephaly- a rare case of neglected child with enlarging head size

  • Shefali P Assistant Professor, Department of Paediatrics, East Point College of Medical Sciences and Research Centre, Bangalore,Karnataka, India
  • B Sandeep Professor, Department of Paediatrics, East Point College of Medical Sciences and Research Centre, Bangalore, Karnataka,India
  • B Kiran HOD & Professor, Department of Paediatrics, East Point College of Medical Sciences and Research Centre, Bangalore, Karnataka,India
Keywords: Key words- Hydrancephaly, cerebrospinal fluid, hydrocephalous, internal carotid artery occlusion

Abstract

Hydranencephaly is a rare congenital abnormality characterized by the absence and replacement ofthe cerebral hemisphere by cerebrospinal fluid. Here we report a rare case of a child who presentedvery late at 2 years of age with a massively enlarged head size with spasticity of all four limbs,suspected of hydrocephalous at first while on further work up diagnosed to have hydranencephaly.This report is aimed to make clinicians aware of a rare condition which can present very late even upto 2 years of age.

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References

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How to Cite
Dr. Shefali Patel, B Sandeep, & B Kiran. (2022). Hydranencephaly- a rare case of neglected child with enlarging head size. Pediatric Review: International Journal of Pediatric Research, 9(5), 34-37. Retrieved from https://pediatrics.medresearch.in/index.php/ijpr/article/view/728
Section
Case Report