Childhood Hypertrophic Cardiomyopathy with Double Chambered Right ventricle: A rare coexistence
A rare coexistence
Abstract
The prevalence of hypertrophic cardiomyopathy (HCM) is about 0.05-0.2% of the general population. The occurrence of HCM is a significant cause of sudden cardiac death in any age group and cause of heart failure. The generally accepted definition of HCM is a disease state characterised by unexplained left ventricular (LV) hypertrophy without dilatation of ventricular chambers in the absence of another cardiac or systemic disease, which itself is capable of producing the amplitude of hypertrophy, caused by a genetic disorder in one of the at least ten genes that encode the proteins of the cardiac sarcomere. The prevalence of double chambered right ventricle (DCRV) with childhood HCM is unknown and extremely rare. We are presenting here a unique coexistence of HCM with severe left ventricular outflow (LVOT) obstruction and DCRV in a 5year old male child.
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References
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Copyright (c) 2023 Author (s). Published by Siddharth Health Research and Social Welfare Society
This work is licensed under a Creative Commons Attribution 4.0 International License.
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